Fulminant demyelinating neuropathy mimicking cerebral death.
Autor(es)Bakshi N.; Maselli R. A.; Gospe S. M.; Ellis W. G.; McDonald C.; Mandler R. N.
ResumoGuillain-Barré syndrome can very rarely present with acute quadripares and cranial nerve involvement resembling a locked-in state. We describe a very unusual case of fulminant neuropathy in a child who was previously exposed to vincristine. The clinical picture resembled brain death; however, electrodiagnostic studies led to the diagnosis of a peripheral neuropathy. Serial electrodiagnostic studies and pathologic findings confirmed demyelination.
ImprentaMuscle & Nerve, v. 20, n. 12, p. 1595-1597, 1997
Identificador do Objeto Digital10.1002/(SICI)1097-4598(199712)20:12<1595::AID-MUS17>3.0.CO;2-#
DescritoresGuillain-Barre Syndrome - Cytopathology ; Guillain-Barre Syndrome - Proteins ; Guillain-Barre Syndrome - Antibodies
Data de Publicação:1997