Autor(es)Boukhris S,Magy L,Li Y,Debras C,Vallat J-M

ResumoInvolvement of the autonomic nervous system during Chronic Inflammatory Demyelinating Polyneuropathy (CIDP) is rare. Localised hyperhydrosis and Claude Bernard Horner (CBH) syndrome have never been reported in patients with CIDP. We report the case of a 65-year-old right handed man who presented with hyperhydrosis localised to the right hemithorax and hemiface and a left CBH syndrome. After an extensive workup, the patient was found to have CIDP as the only cause of autonomic nervous system involvement. The symptoms resolved slowly after three courses of intravenous immunoglobulins. Signs of autonomic nervous system involvement can be observed in CIDP as in Guillain-Barré syndrome. This case report shows that immunomodulatory treatment can be effective against dysautonomia in CIDP.

Palavras-ChaveChronic inflammatory demyelinating polyneuropathy (CIDP); Claude Bernard Horner syndrome; Hyperhydrosis; Autonomous nervous system

ImprentaRevue Neurologique, v. 161, n. 12 Pt 1, p. 1228-1231, 2005

DescritoresGuillain-Barre Syndrome - Pathogenesis

Data de Publicação:2005